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https://doi.org/10.15690/onco.v3i4.1630

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Аннотация

В 2002 г. в Международной классификации опухолей костей и мягких тканей было выделено семейство мезенхимальных опухолей, обозначенных общим термином «пекомы» (PEComas). Обзор литературных данных подтверждает трудности в диагностике и отсутствие прогресса в лечении больных. Несмотря на достижения в области изучения пеком, гистологическая природа этих неоплазий остается неясной. Требуется дальнейшее изучение прогностических факторов для проведения адекватного лечения. Больные, получившие лечение по поводу пеком различных локализаций, требуют тщательного динамического наблюдения независимо от потенциала опухоли, так как возможно развитие поздних рецидивов и метастазов. 

Об авторе

И. В. Нечушкина
Российский онкологический научный центр им. Н.Н. Блохина Минздрава России
Россия

Нечушкина Инесса Викторовна, доктор медицинских наук, профессор кафедры детской онкологии ФГБОУ ДПО РМАНПО Минздрава России, детский онколог хирургического отделения № 2 НИИ детской онкологии и гематологии РОНЦ им. Н.Н. Блохина

Адрес: Москва, Каширское шоссе, д. 23



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Для цитирования:


Нечушкина И.В. ПЕКОМЫ. Онкопедиатрия. 2016;3(4):267-276. https://doi.org/10.15690/onco.v3i4.1630

For citation:


Nechushkina I.V. PEComa. Oncopediatrics. 2016;3(4):267-276. (In Russ.) https://doi.org/10.15690/onco.v3i4.1630

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